Rare disease projects

The BioResource has built patient cohorts, including relatives, for more than 60 rare diseases.

The table below lists each rare disease cohort, the number of (active?) participants, how many have completed a Clinical Report Form (CRF), and whether participants are adult, paediatric or both.

All groups are available for recall studies.

If you have any questions, please email: rarediseases@bioresource.nihr.ac.uk.

Project codeRare disease projectParticipantsCRFs completedAdult/Paediatric/Both
RDC-AATAlph-1 Antitrypsin Deficiency246213both
RDC-ACHAchondroplasia and Hypochondroplasia2222both
RDC-AIHAutoimmune Hepatitis362334both
RDC-AIVAutoimmune Vasculitis448409adults
RDC-AMCArthrogryposis7170both
RDC-ANDRare Autoimmune Neurological Disease3636adults
RDC-AODAortic Dissection101100adults
RDC-ATGAtaxia Telangiectasia99both
RDC-BCARefractoriness First-line Treatment for Blood Cell Autoimmunity560548both
RDC-BCRBirdshot Chorioretinopathy7573adults
RDC-BPDBleeding, Thrombotic and Platelet Disorders3356464both
RDC-CFTCystic Fibrosis13671361both
RDC-CHGCHARGE Syndrome33paeds
RDC-CHICongenital Hyperinsulinism1110paeds
RDC-CILCiliopathies: Bardet Biedl and Alström Syndrome8742both
RDC-CKDPregnancy in Chronic Kidney Disease229229adults
RDC-CRDChromatin Disorders96both
RDC-CSVCerebral Small Vessel Disease30134adults
RDC-CTLCutaneous Lymphoma135101adults
RDC-CYSCystinosis4040adults
RDC-ECTMultiple Endocrine Neoplasia Type 1 and Pancreatic Neuroendocrine Tumours11470both
RDC-FIPFamilial Interstitial Pneumonia7272adults
RDC-GCAGiant Cell Arteritis278269adults
RDC-HAEHereditary Angioedema8865adults
RDC-HBPHaemoglobinopathies11881120both
RDC-HCDHistiocytic Disorders1818adults
RDC-HXRHydroxychloroquine Retinopathy1313adults
RDC-IANIgA Nephropathy799750both
RDC-ICPIntrahepatic Cholestasis of Pregnancy323110adults
RDC-IMPImprinting Disorders cohort7154both
RDC-INDRare Inherited Neurological Disorders355309both
RDC-IONInherited Optic Neuropathies139139both
RDC-IRDInherited Retinal Dystrophy1490959both
RDC-JSCJuvenile Systemic Sclerosis66both
RDC-MACOcular Maldevelopment: Microphthalmia, Anophthalmia and Ocular Coloboma145116both
RDC-MBDMonogenic Beta-cell Diabetes6968adults
RDC-MMTMultiple Primary Malignant Tumours77749both
RDC-MNPMembranous Nephropathy1212adults
RDC-NF1Neurofibromatosis type 1444357both
RDC-NF2Neurofibromatosis type 2208197both
RDC-NRCNarcolepsy - Type 1 and Type 24529both
RDC-OCAOculocutaneous Albinism1

RDC-PBCPrimary Biliary Cholangitis278276adults
RDC-PCDPrimary Ciliary Dyskinesia3434adults
RDC-PDCType 2 Diabetes in Children2813both
RDC-PIDPrimary Immunodeficiency2553117both
RDC-PMGMembranoproliferative Glomerulonephritis and C3 Glomerulopathy27621both
RDC-PNDPaediatric Neurodevelopmental Disorders357304both
RDC-PODOvergrowth Disorders154both
RDC-PSCPrimary Sclerosing Cholangitis363352both
RDC-PSJPrimary Sjogrens Syndrome302234adults
RDC-SADSystemic Autoinflammatory Disorders - AOSD and uSAID11587both
RDC-SAPSAPHO (synovitis, acne, pustulosis, hyperostosis, osteitis)121111both
RDC-SHGSevere Hyperemesis Gravidarum226225adults
RDC-SMDStem Cell and Myeloid Disorders27852both
RDC-SODSepto-optic Dysplasia1414both
RDC-SSCSystemic Sclerosis614532adults
RDC-TTATransthyretin Amyloidosis1085579adults
RDC-TUSTurner’s Syndrome131131both
RDC-WOLWolfram Syndrome180both





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